Endolymphatic sac tumor

Post contrast T1 weighted MRI demonstrates intense enhancement of both the eye and the endolymphatic sac tumor in patient with VHL.

An endolymphatic sac tumor (ELST) is a very uncommon papillary epithelial neoplasm arising within the endolymphatic sac or endolymphatic duct. This tumor shows a very high association with Von Hippel–Lindau syndrome (VHL).[1]

  1. ^ Heffner DK (Dec 1989). "Low-grade adenocarcinoma of probable endolymphatic sac origin A clinicopathologic study of 20 cases". Cancer. 64 (11): 2292–302. doi:10.1002/1097-0142(19891201)64:11<2292::AID-CNCR2820641119>3.0.CO;2-#. PMID 2804921.