Hypergonadotropic hypogonadism | |
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Other names | Peripheral/gonadal hypogonadism |
Specialty | Endocrinology |
Hypergonadotropic hypogonadism (HH), also known as primary or peripheral/gonadal hypogonadism or primary gonadal failure, is a condition which is characterized by hypogonadism which is due to an impaired response of the gonads to the gonadotropins, follicle-stimulating hormone (FSH) and luteinizing hormone (LH), and in turn a lack of sex steroid production.[1] As compensation and the lack of negative feedback, gonadotropin levels are elevated. Individuals with HH have an intact and functioning hypothalamus and pituitary glands (of the hypothalamic-pituitary-gonadal (HPA) axis) so they are still able to produce FSH and LH.[1] HH may present as either congenital or acquired, but the majority of cases are of the former nature.[2][3] HH can be treated with hormone replacement therapy.[4]