Lymphangioleiomyomatosis

Lymphangioleiomyomatosis (LAM)
Other nameslymphangiomyomatosis, LAM
Figure A shows the location of the lungs and airways in the body. The inset image shows a cross-section of a healthy lung. Figure B shows a view of the lungs with LAM and a collapsed lung (pneumothorax). The inset image shows a cross-section of a lung with LAM.
SpecialtyPulmonology Edit this on Wikidata

Lymphangioleiomyomatosis (LAM) is a rare, progressive and systemic disease that typically results in cystic lung destruction. It predominantly affects women, especially during childbearing years.[1] The term sporadic LAM is used for patients with LAM not associated with tuberous sclerosis complex (TSC), while TSC-LAM refers to LAM that is associated with TSC.[2]

  1. ^ McCormack FX (February 2008). "Lymphangioleiomyomatosis: a clinical update". Chest. 133 (2): 507–16. doi:10.1378/chest.07-0898. PMID 18252917.
  2. ^ "Sporadic lymphangioleiomyomatosis: Clinical presentation and diagnostic evaluation". UpToDate. Retrieved 19 March 2018.