Progressive symmetric erythrokeratodermia

Progressive symmetric erythrokeratodermia
Other namesErythrokeratodermia progressiva symmetrica

Progressive symmetric erythrokeratodermia is a rare, autosomal dominant skin condition that manifests soon after birth with erythematous, hyperkeratotic plaques that are symmetrically distributed on the extremities, buttocks, and face, but sparing the trunk.[1]: 565  No other clinical symptoms nor mental or physical signs are usually associated with the condition.[2]

This condition is also known as Darier-Gottron syndrome, progressive symmetric erythrokeratoderma, progressive symmetric erythrokeratodermia of Gottron and erythrokeratodermia variabilis et progressiva.

Less than one hundred cases have been reported to date.

  1. ^ James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. ISBN 0-7216-2921-0.
  2. ^ Kan; Chung-Hong, Hu; Woan-Ruoh, Lee (2003). Shu-Feng' Progressive Symmetric Erythrokeratodermia - A case report. Dermatol Sinica, June 2003.