Cutis verticis gyrata

Cutis verticis gyrata
Other namesCVG
Cutis verticis gyrata in a congenital imbecile

Cutis verticis gyrata is a medical condition usually associated with thickening of the scalp.[1] The condition is identified by excessive thickening of the soft tissues of the scalp and characterized by ridges and furrows, which give the scalp a cerebriform appearance. Clinically, the ridges are hard and cannot be flattened on applying pressure. Patients show visible folds, ridges or creases on the surface of the top of the scalp.[2] The number of folds can vary from two to roughly ten and they are typically soft and spongy. The condition typically affects the central and rear regions of the scalp, but sometimes can involve the entire scalp.

Hair loss can occur over time where the scalp thickens, though hair within any furrows remains normal. Thus far, due to the (apparent) rarity of the condition, limited research exists and causes are as yet undetermined. What is known, is that the condition is not exclusively congenital.

The condition was first reported by Jean-Louis-Marc Alibert in 1837,[3] who called it cutis sulcata.[4] A clinical description of the condition was provided by Robert[who?] in 1843[5] and it was named by Paul Gerson Unna in 1907.[6] It has also been called Robert-Unna syndrome, bulldog scalp, corrugated skin, cutis verticis plicata, and pachydermia verticis gyrata.[7]

  1. ^ James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology (10th ed.). Saunders. p. 572. ISBN 978-0-7216-2921-6.
  2. ^ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. p. 1502. ISBN 978-1-4160-2999-1.
  3. ^ Tan O, Ergen D (July 2006). "Primary essential cutis verticis gyrata in an adult female patient: a case report". The Journal of Dermatology. 33 (7): 492–5. doi:10.1111/j.1346-8138.2006.00116.x. PMID 16848824. S2CID 19782540.
  4. ^ Georgescu, Simona Roxana; Sârbu, Maria Isabela; Mitran, Cristina Iulia; Mitran, Mădălina Irina; Rusu, Alice; Benea, Vasile; Tampa, Mircea (2016). "Cutis verticis gyrata in a patient with multiple basal cell carcinomas; case presentation and review of the literature". Journal of Mind and Medical Sciences. 3 (1): 80–87.
  5. ^ Skibinska, Malgorzata D.; Janniger, Camila K. (February 2019). "Cutis Verticis Gyrata". Medscape.
  6. ^ Unna, PG (1907). "Cutis verticis gyrata". Monatshefte für praktische Dermatologie (in German). 45 (5): 227–33. OCLC 815639790.
  7. ^ Levine, Norman (2004). Dermatology Therapy A-Z Essentials. Berlin New York: Springer. p. 166. ISBN 978-3-540-00864-4.