Enlarged vestibular aqueduct

Enlarged vestibular aqueduct
Other namesEnlarged vestibular aqueduct, Dilated vestibular aqueduct or Widened vestibular aqueduct
Interior of right osseous labyrinth

Large vestibular aqueduct is a structural deformity of the inner ear. Enlargement of this duct is one of the most common inner ear deformities and is commonly associated with hearing loss during childhood.[1] The term was first discovered in 1791 by Mondini when he was completing a temporal bone dissection. It was then defined by Valvassori and Clemis as a vestibular aqueduct that is greater than or equal to 2.0 mm at the operculum and/or greater than or equal to 1.0 mm at the midpoint.[2] Some use the term enlarged vestibular aqueduct syndrome, but this is felt by others to be erroneous as it is a clinical finding which can occur in several syndromes.[citation needed]

  1. ^ S. Usami; Satoko Abe; Mike D. Weston; Hideichi Shinkawa; Guy Van Camp; William J. Kimberling (1999), "Non-syndromic hearing loss associated with enlarged vestibular aqueduct is caused by PDS mutations", Human Genetics, 104 (2): 188–192, doi:10.1007/s004390050933, PMID 10190331, S2CID 3116063
  2. ^ Yang, Christina (2016). "Vestibular Pathology in Children with enlarged vestibular aqueduct". The Laryngoscope. 126 (10): 2344–50. doi:10.1002/lary.25890. PMID 26864825.