Ketotic hypoglycemia refers to any circumstance in which low blood glucose is accompanied by ketosis, the presence of ketone bodies (such as beta-hydroxybutyrate) in the blood or urine. This state can be either physiologic or pathologic; physiologic ketotic hypoglycemia is a common cause of hypoglycemia in children, often in response to stressors such as infection or fasting.[1] Pathologic ketotic hypoglycemia is typically caused by metabolic defects, such as glycogen storage disorders.[2]
^Kliegman RW, Nelson WE, eds. (2020). Nelson Textbook of Pediatrics. Vol. 2 (21st ed.). Philadelphia, Pa: Elsevier. ISBN978-0-323-52950-1.