Scimitar syndrome

Scimitar syndrome
Scimitar syndrome chest CT
SpecialtyMedical genetics Edit this on Wikidata

Scimitar syndrome, or congenital pulmonary venolobar syndrome, is a rare congenital heart defect characterized by anomalous venous return from the right lung (to the systemic venous drainage, rather than directly to the left atrium).[1] This anomalous pulmonary venous return can be either partial (PAPVR) or total (TAPVR). The syndrome associated with PAPVR is more commonly known as Scimitar syndrome after the curvilinear pattern created on a chest radiograph by the pulmonary veins that drain to the inferior vena cava.[2] This radiographic density often has the shape of a scimitar, a type of curved sword.[2] The syndrome was first described by Catherine Neill in 1960.[3]

  1. ^ Sehgal, Arvind; Loughran-Fowlds, Allison, Clinical Brief: Scimitar Syndrome (PDF), medIND — Biomedical journals from India, archived from the original (PDF) on 2009-05-30, retrieved 2008-02-28
  2. ^ a b Scimitar Syndrome, Children's Hospital Boston, archived from the original on 2010-12-04, retrieved 2008-02-28
  3. ^ Oransky, Ivan (2006). "Catherine Neill" (PDF). The Lancet. 367 (9519): 1312. doi:10.1016/s0140-6736(06)68565-6. S2CID 205947768.