Sp100 nuclear antigen

SP100 nuclear antigen
Identifiers
SymbolSP100
NCBI gene6672
HGNC11206
OMIM604585
RefSeqNM_003113
UniProtP23497
Other data
LocusChr. 2 q37.1
Search for
StructuresSwiss-model
DomainsInterPro

Sp100 nuclear antigen is an interferon stimulated antigen found in the cell nuclei of many human and higher animal cells. Autoantibodies directed against Sp100 are often found in patients with primary biliary cirrhosis.[1] Histologically Sp100 'dots' regions of the cell nucleus. Viral infection and mitogens affect the expression of the Sp100 autoantigen. Cells grown in the presence of interferons (α, β, and γ) revealed an increase both in size and number of the Sp100 protein-containing nuclear dots and increase the protein concentration. This raises "the question whether cytokine-mediated increase of Sp100 protein expression plays a role in induction of anti-Sp100 autoantibodies."[2]

  1. ^ Szostecki C, Guldner HH, Netter HJ, Will H (1990). "Isolation and characterization of cDNA encoding a human nuclear antigen predominantly recognized by autoantibodies from patients with primary biliary cirrhosis". J. Immunol. 145 (12): 4338–47. doi:10.4049/jimmunol.145.12.4338. PMID 2258622. S2CID 43572051.
  2. ^ Guldner HH, Szostecki C, Grötzinger T, Will H (1992). "IFN enhance expression of Sp100, an autoantigen in primary biliary cirrhosis". J. Immunol. 149 (12): 4067–73. doi:10.4049/jimmunol.149.12.4067. PMID 1281200. S2CID 20921655.